Congenital hypertrophic pyloric stenosis

This code identifies a congenital narrowing of the pylorus, the opening from the stomach to the small intestine, caused by an overgrowth of the muscle surrounding it. This condition obstructs the passage of food, leading to characteristic symptoms in infants.

Apply this code for infants diagnosed with hypertrophic pyloric stenosis present at birth. Documentation should clearly indicate the congenital nature of the condition, often evidenced by projectile vomiting and an olive-shaped mass palpable in the abdomen.

• Ensure documentation specifies "congenital" to differentiate from acquired pyloric stenosis, which is rare in infants.
• This diagnosis often necessitates surgical intervention (pyloromyotomy); code the procedure separately.
• Do not confuse with other causes of infant vomiting or feeding difficulties without confirmed pyloric hypertrophy.