Congenital hypertrophic pyloric stenosis

This code represents a congenital narrowing of the pylorus, the opening from the stomach to the small intestine, due to thickening of the muscle. This condition obstructs the passage of food, leading to forceful vomiting in infants. It is present at birth, though symptoms typically manifest a few weeks later.

Use this code for infants diagnosed with hypertrophic pyloric stenosis that is present from birth. Documentation should clearly indicate the congenital nature of the condition, often supported by ultrasound findings showing pyloric muscle thickening and elongation, and clinical signs like projectile vomiting.

• Ensure documentation specifies "congenital" to differentiate from acquired forms, though acquired pyloric stenosis is rare in infants.
• Do not confuse with other causes of infant vomiting or gastrointestinal obstruction.
• Sequence as the primary diagnosis when it is the reason for the encounter, such as for surgical correction (pyloromyotomy).