Tracheoesophageal fistula, esophageal atresia and stenosis

This code represents a congenital anomaly involving the esophagus and trachea. It specifically describes conditions where the esophagus is not fully formed (atresia), narrowed (stenosis), or has an abnormal connection to the trachea (fistula). These defects often occur together and manifest shortly after birth.

Use this code for newborns or infants diagnosed with congenital tracheoesophageal fistula, esophageal atresia, or congenital esophageal stenosis. Documentation should clearly specify the presence of one or more of these conditions, typically identified through imaging studies (e.g., esophagram) and clinical presentation (e.g., choking, regurgitation, respiratory distress).

• Always look for specific documentation of the type of atresia or fistula (e.g., Type C, H-type) if available, though this code is broad enough for general use.
• Consider additional codes for associated congenital anomalies, as these conditions often co-occur with other birth defects.
• Ensure the documentation specifies "congenital" to differentiate from acquired fistulas or strictures.