Congenital hiatus hernia

This code signifies a birth defect where a portion of the stomach protrudes through an opening in the diaphragm into the chest cavity. This congenital anomaly results from incomplete closure or malformation of the diaphragm during fetal development.

Apply this code for newborns or infants diagnosed with a hiatus hernia present at birth. Documentation should clearly state "congenital hiatus hernia" or describe a diaphragmatic defect allowing stomach herniation, identified shortly after birth.

• Differentiate from acquired hiatus hernia, which would be coded differently.
• Consider additional codes for associated congenital anomalies or symptoms, such as respiratory distress.
• Ensure documentation specifies the congenital nature, as opposed to an unspecified or acquired diaphragmatic hernia.