Congenital factor VIII disorder

This code signifies a hereditary deficiency or abnormality of coagulation factor VIII, leading to impaired blood clotting. It is most commonly associated with Hemophilia A, an X-linked recessive bleeding disorder characterized by spontaneous or prolonged bleeding episodes. The severity of the disorder depends on the level of functional factor VIII.

Use this code for patients diagnosed with congenital factor VIII deficiency, including all forms of Hemophilia A. Documentation should clearly state the diagnosis of Hemophilia A or a specific congenital factor VIII disorder, often confirmed by laboratory testing showing reduced factor VIII activity. This code is appropriate for initial diagnoses, follow-up care, and management of bleeding episodes related to the condition.

• Do not confuse with acquired factor VIII inhibitors, which would be coded differently.
• Always sequence this code as the primary diagnosis when it is the reason for the encounter.
• Consider additional codes for specific manifestations or complications of hemophilia, such as hemarthrosis.