Congenital deficiency of other clotting factors

This code signifies a hereditary bleeding disorder caused by a quantitative or qualitative defect in a clotting factor other than Factor VIII (hemophilia A) or Factor IX (hemophilia B). These deficiencies can lead to impaired hemostasis, resulting in easy bruising, prolonged bleeding after injury or surgery, or spontaneous hemorrhages. The specific factor involved is not specified by this code, but it excludes the most common hemophilias.

Use this code when documentation specifies a congenital deficiency of a clotting factor such as Factor I (fibrinogen), Factor II (prothrombin), Factor V, Factor VII, Factor X, Factor XI, or Factor XIII. It is appropriate when the genetic basis of the deficiency is known or strongly suspected from birth. Supporting documentation should include laboratory findings confirming the specific factor deficiency.

• Do not use this code for acquired clotting factor deficiencies; those have separate codes.
• If the specific congenital factor deficiency (e.g., congenital Factor VII deficiency) is known and has a more precise ICD-9-CM code, use that specific code instead.
• Always review the medical record for laboratory results and physician notes detailing the specific factor involved to ensure the most accurate code is selected.