Von Willebrand's disease

This code represents Von Willebrand's disease, a common inherited bleeding disorder caused by a deficiency or dysfunction of von Willebrand factor (VWF). VWF is a protein crucial for platelet adhesion and aggregation, as well as for protecting factor VIII from degradation. Patients typically present with mucocutaneous bleeding symptoms, such as epistaxis, menorrhagia, and easy bruising.

Use this code for patients diagnosed with any type of Von Willebrand's disease, confirmed by laboratory testing showing abnormal VWF levels or function. This includes Type 1 (partial quantitative deficiency), Type 2 (qualitative defects), and Type 3 (severe quantitative deficiency). Documentation should clearly state the diagnosis of Von Willebrand's disease and may specify the type if known.

• Do not confuse with other coagulation defects; ensure documentation specifically mentions Von Willebrand's disease.
• If the specific type of Von Willebrand's disease (e.g., Type 1, Type 2, Type 3) is documented, this code is still appropriate as ICD-9-CM does not offer more granular codes for the types.
• Code any associated bleeding manifestations or complications separately, if applicable.