Hereditary factor VIII deficiency

This code identifies a congenital bleeding disorder characterized by a deficiency in coagulation factor VIII, leading to impaired blood clotting. It is commonly known as hemophilia A, the most prevalent form of hemophilia. Patients typically experience spontaneous or prolonged bleeding episodes.

Assign this code when documentation confirms a diagnosis of hereditary factor VIII deficiency, such as hemophilia A. This includes cases diagnosed through genetic testing, coagulation factor assays showing reduced factor VIII activity, and a clinical history consistent with the disorder.

• Ensure the documentation specifies "hereditary" or "congenital" to differentiate from acquired factor VIII deficiency.
• Do not use this code if the documentation indicates factor VIII deficiency with a vascular defect; refer to the Excludes1 note.
• Code any associated bleeding manifestations or complications separately, following sequencing guidelines.