Sjogren syndrome with other organ involvement

This code signifies Sjögren's syndrome where the autoimmune disease has progressed beyond sicca symptoms (dry eyes, dry mouth) to affect other organ systems. This can include manifestations such as interstitial lung disease, vasculitis, neuropathy, or renal tubular acidosis.

Use this code when documentation explicitly states Sjögren's syndrome with involvement of an organ system other than the exocrine glands typically affected. This requires physician documentation detailing the specific extra-glandular manifestation, such as "Sjögren's syndrome with interstitial nephritis" or "Sjögren's syndrome with peripheral neuropathy."

• Always ensure the medical record clearly specifies the "other organ involvement" to justify this code.
• Do not use this code for Sjögren's syndrome limited to sicca symptoms; use M35.00 or M35.01 for those cases.
• Code the specific extra-glandular manifestation (e.g., interstitial lung disease, vasculitis) as an additional diagnosis to provide further specificity.