Sjogren syndrome, unspecified

This code represents an autoimmune disorder characterized by chronic inflammation of exocrine glands, primarily the lacrimal and salivary glands, leading to sicca symptoms (dry eyes and dry mouth). It can also affect other organs and systems, causing widespread systemic manifestations.

Use this code when the provider documents "Sjogren syndrome" without further specification of primary or secondary type. This is appropriate when the diagnostic workup is incomplete or the specific type cannot be determined from the available clinical information. Documentation should clearly indicate a diagnosis of Sjogren syndrome.

• Do not use this code if the documentation specifies "primary Sjogren syndrome" (M35.01) or "secondary Sjogren syndrome" (M35.02).
• Code associated manifestations, such as keratoconjunctivitis sicca (H16.22-) or xerostomia (K11.7), as additional diagnoses.
• Ensure the medical record supports the diagnosis of Sjogren syndrome, even if the specific type is not identified.