Sjogren syndrome with keratoconjunctivitis

This code identifies a systemic autoimmune disorder characterized by chronic inflammation of exocrine glands, specifically presenting with dry eyes due to inflammation of the lacrimal glands. It signifies the ocular manifestation of Sjögren syndrome, where the immune system attacks moisture-producing glands.

Apply this code when documentation confirms a diagnosis of Sjögren syndrome with specific mention of keratoconjunctivitis sicca or dry eyes attributed to the condition. This is appropriate when the patient exhibits symptoms such as chronic dry, gritty, or burning eyes, and diagnostic tests support both Sjögren syndrome and its ocular involvement.

• Ensure documentation clearly links the keratoconjunctivitis to Sjögren syndrome, rather than other causes of dry eye.
• Do not use this code if keratoconjunctivitis is present but not explicitly attributed to Sjögren syndrome; consider codes for other forms of keratoconjunctivitis.
• Always sequence this code as the primary diagnosis if the keratoconjunctivitis is the reason for the encounter, or as a secondary diagnosis when managing other manifestations of Sjögren syndrome.