Other amyloidosis

This code represents forms of amyloidosis that are not specifically classified elsewhere, indicating the abnormal deposition of insoluble protein fibrils in various tissues and organs. These deposits can lead to organ dysfunction and a range of clinical manifestations depending on the affected systems. It encompasses rare or atypical types of amyloidosis beyond the more common AL, AA, ATTR, or Aβ2M forms.

Use this code when documentation specifies a type of amyloidosis that does not have a more specific ICD-10-CM code, such as ALECT2 amyloidosis, gelsolin amyloidosis, or apolipoprotein A-I amyloidosis. Supporting documentation should clearly identify the specific type of amyloidosis or confirm it is an "other specified" form after ruling out more common types.

• Always seek more specific codes for amyloidosis (e.g., AL, AA, ATTR) if the documentation allows.
• Ensure the medical record clearly identifies the specific type of "other" amyloidosis to justify this code.
• Code any associated organ manifestations (e.g., cardiomyopathy, nephropathy) as secondary diagnoses.