Atypical chronic myeloid leukemia, BCR/ABL-neg, in remission

This code signifies a diagnosis of atypical chronic myeloid leukemia (aCML) that is negative for the BCR/ABL fusion gene, and the patient is currently in a state of remission. aCML is a rare myelodysplastic/myeloproliferative neoplasm characterized by features overlapping with both CML and myelodysplastic syndromes, but without the Philadelphia chromosome.

Apply this code when documentation explicitly states a diagnosis of atypical CML, BCR/ABL-negative, and confirms the patient's current remission status. This typically follows successful treatment, such as chemotherapy or stem cell transplant, and is supported by laboratory findings indicating no evidence of active disease.

• Ensure documentation clearly specifies "atypical" CML and "BCR/ABL-negative" to differentiate from classic CML.
• Confirm the patient's current remission status; if active disease is present, a different code from the C92.2 category would be appropriate.
• Do not confuse with CML, BCR/ABL-positive (C92.1-), or other myelodysplastic/myeloproliferative neoplasms.