Lymp-rich Hodgkin lymphoma, extranodal and solid organ sites

This code represents a specific subtype of Hodgkin lymphoma, characterized by a predominance of lymphocytes and a scarcity of Reed-Sternberg cells, occurring in sites outside of the lymph nodes. It signifies a diagnosis of lymphocyte-rich classical Hodgkin lymphoma affecting organs or tissues other than lymphatic structures.

Use this code when documentation explicitly states a diagnosis of "lymphocyte-rich Hodgkin lymphoma" and specifies an extranodal or solid organ involvement. This applies to cases where the primary tumor site is, for example, the bone marrow, liver, or gastrointestinal tract, rather than a lymph node.

• Ensure the pathology report confirms the "lymphocyte-rich" subtype of Hodgkin lymphoma.
• Verify that the documented site of involvement is clearly extranodal or a solid organ.
• Do not confuse with other Hodgkin lymphoma subtypes or nodal involvement, which have distinct codes.