Congenital mitral stenosis

This code represents a congenital heart defect characterized by a narrowing of the mitral valve, which obstructs blood flow from the left atrium to the left ventricle. This stenosis is present at birth and can vary in severity, impacting cardiac function and potentially leading to heart failure if uncorrected.

Use this code for diagnoses of mitral valve narrowing that is identified as being present from birth. Documentation should clearly state "congenital mitral stenosis" or describe a mitral valve obstruction with an explicit congenital etiology. This code is appropriate for initial diagnosis, follow-up, and management of this specific congenital anomaly.

• Differentiate from acquired mitral stenosis (e.g., rheumatic heart disease), which is coded differently.
• Always review documentation for laterality if specified, though mitral stenosis is typically a single valve issue.
• Consider sequencing with codes for associated congenital heart defects or complications, such as heart failure.