Tricuspid atresia and stenosis, congenital

This code signifies a congenital heart defect characterized by the absence or abnormal narrowing of the tricuspid valve, preventing blood flow from the right atrium to the right ventricle. This condition often leads to a hypoplastic right ventricle and requires an atrial septal defect or patent foramen ovale for survival.

Apply this code for diagnoses of tricuspid atresia or congenital tricuspid stenosis documented in a patient's medical record. Supporting documentation should clearly indicate the congenital nature of the valve anomaly, typically identified in infancy or early childhood.

• Differentiate from acquired tricuspid stenosis, which would be coded elsewhere.
• Always look for associated congenital heart defects, such as atrial septal defects or ventricular septal defects, and code them separately.
• Ensure documentation specifies "congenital" to avoid miscoding with other forms of tricuspid valve disease.