Congenital stenosis of aortic valve

This code signifies a birth defect characterized by a narrowing of the aortic valve, the main outflow valve from the heart. This congenital malformation obstructs blood flow from the left ventricle to the aorta, potentially leading to increased cardiac workload and reduced systemic perfusion.

Apply this code when documentation clearly indicates a diagnosis of congenital aortic valve stenosis. This is typically supported by echocardiogram findings, cardiac catheterization reports, and physician notes detailing the presence of a narrowed aortic valve from birth.

• Differentiate from acquired aortic stenosis (e.g., rheumatic, degenerative), which would be coded differently.
• Look for specific terms like "congenital," "birth defect," or "present at birth" in relation to the aortic valve stenosis.
• Consider sequencing this code as a primary diagnosis when it is the main reason for the encounter or hospitalization.