Early congenital syphilis, symptomatic

This code represents congenital syphilis manifesting with clinical signs and symptoms in an infant, typically within the first two years of life. These symptoms can be diverse, affecting multiple organ systems, and are a direct result of transplacental transmission of Treponema pallidum.

Use this code when documentation confirms a diagnosis of syphilis in an infant with active clinical manifestations, such as hepatosplenomegaly, rash, rhinitis (snuffles), bone lesions, or central nervous system involvement. Serological evidence of syphilis in both the infant and mother, along with clinical findings, supports this diagnosis.

• Distinguish from late congenital syphilis (090.4x) which presents after two years of age.
• Always sequence this code as the primary diagnosis when it is the reason for the encounter.
• Ensure documentation clearly specifies "symptomatic" to differentiate from asymptomatic early congenital syphilis (090.1).