Early mucocutaneous congenital syphilis

This code signifies the presence of syphilis acquired congenitally, manifesting in its early stages with mucocutaneous lesions. These lesions typically appear within the first two years of life and can include maculopapular rashes, condylomata lata, or mucous patches. It indicates an active, symptomatic infection transmitted from mother to child during pregnancy.

Use this code when documentation clearly states a diagnosis of congenital syphilis with active mucocutaneous manifestations occurring in an infant or young child. Supporting documentation should include a positive serological test for syphilis in the infant and/or mother, along with a description of characteristic skin or mucous membrane lesions. This code is appropriate for initial diagnosis and treatment of early symptomatic congenital syphilis.

• Differentiate from late congenital syphilis (A50.5x) which presents with different clinical features and later onset.
• Ensure documentation specifies "early" and "mucocutaneous" to support this specific subcategory.
• Sequence this code as the primary diagnosis when it is the reason for the encounter.