Other cystic kidney diseases

This code represents various non-specific cystic kidney disorders that do not fit into more defined categories of polycystic kidney disease or other specified cystic renal conditions. It encompasses a range of congenital or acquired renal cystic formations not otherwise classified.

Use this code when documentation indicates the presence of renal cysts that are not identified as autosomal dominant polycystic kidney disease (ADPKD), autosomal recessive polycystic kidney disease (ARPKD), medullary cystic kidney disease, or other specified cystic renal conditions. This code is appropriate when the physician's diagnosis explicitly states "other cystic kidney disease" or describes a cystic renal condition that lacks a more specific ICD-10-CM code.

• Ensure documentation clearly differentiates from specific types of polycystic kidney disease (e.g., ADPKD, ARPKD) which have their own codes.
• Avoid using this code if a more specific diagnosis, such as simple renal cyst (N28.1), is documented.
• Query the provider for further specificity if the documentation is vague regarding the type of cystic kidney disease.