Congenital multiple renal cysts

This diagnosis code identifies a congenital condition characterized by the presence of multiple fluid-filled sacs within the kidneys from birth. It signifies a non-hereditary form of renal cystic disease where numerous cysts develop in both kidneys, often leading to renal dysfunction.

Apply this code when documentation explicitly states "congenital multiple renal cysts" or "multiple renal cysts, congenital origin." This is appropriate for newborns or infants diagnosed with this specific congenital anomaly, distinct from inherited polycystic kidney diseases. Supporting documentation should include imaging reports confirming multiple renal cysts and a clear indication of their congenital nature.

• Differentiate from autosomal dominant polycystic kidney disease (ADPKD) and autosomal recessive polycystic kidney disease (ARPKD), which have specific codes.
• Ensure the documentation specifies "multiple" cysts; a single congenital renal cyst would be coded differently.
• Consider sequencing with any associated signs, symptoms, or complications, such as chronic kidney disease, if present.