Other polycystic kidney, infantile type

This code signifies a congenital disorder characterized by the presence of multiple cysts within the kidneys, specifically an infantile form that does not precisely fit the criteria for autosomal recessive polycystic kidney disease (ARPKD) or other specified types. It represents a spectrum of cystic kidney diseases presenting in infancy, distinct from adult-onset polycystic kidney disease.

Apply this code when documentation indicates a diagnosis of polycystic kidney disease in an infant, and the specific type is identified as "infantile type" but not further specified as ARPKD or another distinct form. This code is appropriate when the clinical presentation and imaging findings are consistent with infantile polycystic kidneys, but a more precise sub-classification is not provided or does not apply.

• Ensure documentation clearly specifies "infantile type" and rules out other specific forms of polycystic kidney disease, such as ARPKD (Q61.4).
• Do not use this code for adult polycystic kidney disease (e.g., Q61.2, Q61.3).
• Consider sequencing this code as the primary diagnosis when it is the reason for the encounter, or as a secondary diagnosis if it is a co-morbidity impacting care.