Hypospadias, perineal

This code represents a congenital anomaly of the male urethra where the opening is located on the perineum, posterior to the scrotum. This is a severe form of hypospadias, characterized by a significantly displaced urethral meatus. It often presents with a deeply clefted scrotum and a severely curved penis (chordee).

Use this code for documented cases of hypospadias where the urethral opening is specifically identified as being on the perineum. This diagnosis is typically made at birth or during early childhood examinations. Supporting documentation should clearly specify the location of the meatus as perineal.

• Differentiate from other hypospadias codes based on the precise location of the urethral meatus (e.g., glandular, penile, penoscrotal).
• Code any associated anomalies, such as chordee (Q54.4) or cryptorchidism, separately if documented.
• Ensure the physician's documentation explicitly states "perineal hypospadias" or describes the meatus as being on the perineum.