Congenital hypoplasia and dysplasia of lung

This code describes a developmental abnormality of the lung where it is either underdeveloped (hypoplasia) or abnormally formed (dysplasia) from birth. These conditions result in reduced lung volume and impaired respiratory function.

Use this code for congenital conditions where the lung tissue is structurally incomplete or malformed, leading to chronic respiratory issues. Documentation should clearly state "congenital hypoplasia of lung" or "congenital dysplasia of lung," often identified through imaging studies or at birth.

• Do not use this code if the pulmonary hypoplasia is explicitly linked to prematurity or short gestation; refer to the Excludes1 note.
• Ensure the documentation specifies "congenital" to differentiate from acquired lung conditions.
• Consider additional codes for associated congenital anomalies or resulting respiratory failure.