Congenital bronchiectasis

This code represents a chronic, irreversible dilation of the bronchi and bronchioles that is present at birth. It results in impaired mucociliary clearance, leading to recurrent respiratory infections, chronic cough, and sputum production. The condition is often associated with other congenital anomalies or genetic disorders.

Use this code when documentation explicitly states a diagnosis of congenital bronchiectasis. This diagnosis is typically made in infancy or early childhood based on clinical presentation, imaging studies (e.g., CT scan showing bronchial dilation), and exclusion of acquired causes. Documentation should clearly indicate the congenital origin of the bronchiectasis.

• Differentiate from acquired bronchiectasis, which has different underlying causes and is coded elsewhere.
• Always look for and code any associated congenital anomalies or underlying genetic conditions, as these often coexist.
• Ensure the medical record specifies "congenital" to support the use of this specific code.