Agenesis, hypoplasia, and dysplasia of lung

This code describes congenital malformations of the lung characterized by incomplete development or absence of lung tissue. This can range from complete absence of a lung (agenesis) to underdeveloped lung tissue (hypoplasia) or abnormal cellular organization (dysplasia), impacting respiratory function.

Use this code for documented cases of congenital lung anomalies identified prenatally or postnatally. It is appropriate when imaging studies (e.g., ultrasound, CT, MRI) and clinical findings confirm a diagnosis of agenesis, hypoplasia, or dysplasia of the lung.

• Differentiate between primary congenital lung malformations and acquired lung conditions.
• Ensure documentation specifies the type of malformation (agenesis, hypoplasia, or dysplasia) and laterality if applicable.
• Consider additional codes for associated congenital anomalies or respiratory complications.