Rapidly progressive nephritic syndrome with C3 glomrlneph

This code signifies a severe and rapidly worsening form of kidney inflammation characterized by the presence of C3 glomerulonephritis. This condition involves the immune system attacking the kidney's filtering units, leading to a swift decline in kidney function. It is distinct from other forms of rapidly progressive nephritic syndrome by the specific involvement of C3 complement protein deposits.

Apply this code when documentation explicitly states "rapidly progressive nephritic syndrome" in conjunction with "C3 glomerulonephritis." This diagnosis is typically confirmed by kidney biopsy showing C3 deposits and clinical evidence of rapid renal deterioration, such as acute kidney injury, hematuria, and proteinuria. Ensure the physician's notes clearly differentiate this from dense deposit disease.

• Do not code this with N01.6 (Rapidly progressive nephritic syndrome with dense deposit disease) due to the Excludes1 note.
• Confirm that the documentation specifies C3 glomerulonephritis, not just general glomerulonephritis, for accurate coding.
• Consider sequencing this code as the primary diagnosis when it is the main reason for the encounter and treatment.