Rapidly progr neph synd w focal and seg glomerular lesions

This code signifies a severe and rapidly worsening form of kidney inflammation characterized by the presence of focal and segmental damage to the glomeruli. It indicates a swift decline in kidney function, often leading to kidney failure if untreated.

Assign this code when documentation explicitly states "rapidly progressive nephritic syndrome" and specifies "focal and segmental glomerular lesions" as the underlying pathology. This typically occurs in cases of crescentic glomerulonephritis where less than 50% of glomeruli are affected, or where only parts of the glomeruli are damaged.

• Ensure documentation specifies both "rapidly progressive" and the "focal and segmental" nature of the lesions; otherwise, a more general code may be appropriate.
• Distinguish from N01.0 (diffuse mesangial proliferative glomerulonephritis) or N01.2 (diffuse membranous glomerulonephritis) which describe different lesion patterns.
• Always code the underlying cause of the nephritic syndrome, if known, as a secondary diagnosis.