Polyarteritis with lung involvement [Churg-Strauss]

This code represents Eosinophilic Granulomatosis with Polyangiitis (EGPA), formerly known as Churg-Strauss syndrome. It is a rare systemic vasculitis characterized by asthma, eosinophilia, and granulomatous inflammation affecting small to medium-sized blood vessels, with a prominent impact on the respiratory system.

Use this code for patients diagnosed with EGPA presenting with documented lung involvement, such as asthma, pulmonary infiltrates, or other respiratory manifestations. Documentation should clearly state the diagnosis of Churg-Strauss syndrome or EGPA and specify the presence of lung involvement.

• Ensure documentation explicitly links the polyarteritis to lung involvement.
• Do not confuse with other forms of polyarteritis nodosa (e.g., M30.0) which typically spare the lungs.
• Consider additional codes for specific manifestations or complications, such as asthma (J45.-) or peripheral neuropathy (G60.0).