Wegener's granulomatosis

This code represents Wegener's granulomatosis, a rare, systemic autoimmune disease characterized by inflammation of small and medium-sized blood vessels (vasculitis). It primarily affects the upper and lower respiratory tracts, kidneys, and can involve other organs. Untreated, it can lead to organ damage and be life-threatening.

Use this code for documented cases of Wegener's granulomatosis, also known as Granulomatosis with Polyangiitis (GPA). This diagnosis should be supported by clinical findings, laboratory tests (e.g., positive ANCA), and often biopsy results confirming granulomatous inflammation and vasculitis.

• Ensure documentation clearly specifies Wegener's granulomatosis, not just general vasculitis.
• Code any associated organ manifestations (e.g., renal failure, lung involvement) separately.
• Be aware that in ICD-10-CM, this condition is classified under M31.3.