Juvenile polyarteritis

This code represents a rare, severe form of systemic vasculitis affecting medium-sized arteries, characterized by inflammation and necrosis of the arterial walls, occurring in individuals under 18 years of age. It can lead to aneurysms, thrombosis, and organ damage in various systems, including renal, cardiac, gastrointestinal, and neurological.

Use this code for pediatric patients diagnosed with polyarteritis nodosa (PAN) that manifests before adulthood. Documentation should clearly indicate a diagnosis of polyarteritis and specify the patient's age or an onset of the condition during childhood or adolescence.

• Differentiate from adult-onset polyarteritis nodosa (M30.0) based on the patient's age at diagnosis.
• Code any associated organ manifestations (e.g., renal failure, myocardial infarction) as secondary diagnoses.
• Ensure documentation explicitly states "juvenile" or "childhood onset" polyarteritis to support this specific code.