Yellow nail syndrome

This code represents yellow nail syndrome, a rare disorder characterized by the triad of yellow, thickened nails, lymphedema, and respiratory tract involvement (e.g., pleural effusions, bronchiectasis). The nails typically grow slowly, lack a cuticle, and may be shed.

Assign this code when documentation clearly indicates a diagnosis of yellow nail syndrome. Supporting clinical findings often include characteristic nail changes, evidence of chronic lymphedema, and/or recurrent respiratory issues such as chronic cough or pleural effusions.

• Ensure documentation specifies "syndrome" to differentiate from isolated yellow nails due to other causes.
• Code any associated manifestations, such as lymphedema (e.g., I89.0) or respiratory conditions (e.g., J90, J47.9), as secondary diagnoses.
• Review the patient's medical history for the full diagnostic triad, even if not all components are actively managed during the encounter.