Acquired hemophilia

This diagnosis code represents acquired hemophilia A, a rare autoimmune bleeding disorder characterized by the development of autoantibodies against coagulation factor VIII. It results in spontaneous bleeding episodes, often severe, in individuals with no prior personal or family history of hemophilia.

Use this code for patients presenting with new-onset bleeding symptoms and laboratory findings consistent with factor VIII deficiency, where an inhibitor to factor VIII is detected. Documentation should clearly indicate the acquired nature of the hemophilia, distinguishing it from congenital forms.

• Differentiate carefully from congenital hemophilia A (D66) by reviewing documentation for the presence of factor VIII inhibitors and absence of family history.
• Always sequence this code as the primary diagnosis when it is the reason for the encounter.
• Look for documentation of specific factor VIII inhibitor assays to support the acquired nature of the condition.