Von Willebrand disease, type 2, unspecified

This code represents an inherited bleeding disorder characterized by qualitative defects in von Willebrand factor (VWF), leading to impaired platelet adhesion and aggregation. Type 2 VWD encompasses several subtypes (2A, 2B, 2M, 2N) with varying VWF abnormalities, all resulting in a propensity for mucocutaneous bleeding. This specific code is used when the exact subtype of Type 2 VWD has not been determined or documented.

Use this code for patients diagnosed with Type 2 von Willebrand disease when the medical record does not specify the particular subtype (e.g., 2A, 2B, 2M, 2N). Documentation should clearly indicate a diagnosis of Type 2 VWD, often supported by laboratory findings showing qualitative VWF defects, but without further subtyping. This code is appropriate when the physician has not yet identified the specific variant of Type 2.

• Avoid using this code if the medical record specifies a particular subtype of Type 2 VWD; instead, use the more specific code (e.g., D68.021 for Type 2A).
• Query the provider if "Type 2 VWD" is documented without further specification, to determine if a more precise subtype can be identified.
• This code is for the unspecified type 2 variant; do not confuse it with other types of VWD (e.g., Type 1, Type 3) or acquired von Willebrand syndrome.