Juvenile myelomonocytic leukemia, in remission

This code signifies a diagnosis of juvenile myelomonocytic leukemia (JMML) that is currently in remission. JMML is a rare, aggressive myelodysplastic/myeloproliferative neoplasm primarily affecting young children, characterized by uncontrolled proliferation of myeloid and monocytic cells. Remission indicates a significant reduction or absence of disease signs and symptoms following treatment.

Apply this code when a patient, typically a child, has a documented history of JMML and current clinical and laboratory findings confirm the disease is in remission. This includes situations where the patient is undergoing surveillance after successful treatment, such as chemotherapy or hematopoietic stem cell transplantation. Documentation should clearly state "JMML in remission" or similar terminology.

• Always confirm the "in remission" status is explicitly documented by the physician.
• Do not confuse with active JMML (C93.30) or other types of leukemia.
• Sequence this code as a primary diagnosis when the reason for the encounter is related to the JMML in remission (e.g., follow-up, monitoring).