Juvenile myelomonocytic leukemia, not achieve remission

This code signifies a diagnosis of Juvenile Myelomonocytic Leukemia (JMML), a rare and aggressive myelodysplastic/myeloproliferative neoplasm primarily affecting young children. It specifically indicates that the disease is active and has not yet achieved a state of remission.

Use this code for patients, typically infants or young children, diagnosed with JMML who are currently undergoing treatment or are in an active disease state without evidence of remission. Documentation should clearly state the diagnosis of JMML and confirm the absence of remission, often noted as "active disease" or "not in remission."

• Do not use this code if the patient has achieved complete or partial remission; instead, refer to codes for JMML in remission.
• Always review the pathology report and physician's notes for definitive diagnosis and remission status.
• Consider sequencing this code as the primary diagnosis when it is the reason for the encounter.