Merkel cell carcinoma of other parts of face

This code signifies a rare and aggressive neuroendocrine carcinoma originating from Merkel cells, specifically located on facial areas other than the eyelid. It typically presents as a rapidly growing, firm, painless nodule. The tumor has a high propensity for local recurrence and metastasis.

This code is appropriate for documenting a confirmed diagnosis of Merkel cell carcinoma affecting facial sites such as the cheek, forehead, nose, or chin. Documentation should clearly specify the histological confirmation of Merkel cell carcinoma and the precise facial location. It should be used when the primary tumor is located on the face, excluding the eyelid.

• Ensure the pathology report confirms Merkel cell carcinoma, not another skin malignancy.
• Verify the exact facial location; differentiate from eyelid involvement (C4A.1-).
• Consider sequencing with codes for metastatic disease if applicable, as this cancer frequently metastasizes.