Merkel cell carcinoma of lip

This code signifies a rare and aggressive neuroendocrine carcinoma, Merkel cell carcinoma, specifically originating on the lip. It is characterized by rapid growth and a high propensity for local recurrence and metastasis. This malignancy typically presents as a firm, painless, shiny nodule.

Apply this code when documentation clearly states a diagnosis of Merkel cell carcinoma located on the lip. This diagnosis is typically confirmed by biopsy and histopathological examination. Use this code for primary malignant neoplasms of the lip identified as Merkel cell carcinoma.

• Differentiate carefully from squamous cell carcinoma or basal cell carcinoma of the lip, which are more common.
• Ensure the documentation specifies "Merkel cell carcinoma" and its precise location on the lip, excluding the vermilion border.
• Review pathology reports for definitive diagnosis and specific anatomical site.