Merkel cell carcinoma of nose

This code signifies a rare and aggressive neuroendocrine carcinoma originating from Merkel cells, specifically located on the nose. It is characterized by rapid growth and a high propensity for local recurrence and metastasis.

Apply this code when documentation confirms a pathological diagnosis of Merkel cell carcinoma affecting the nasal region. This includes primary tumors identified on the external nose, nasal cavity, or paranasal sinuses. Supporting documentation should include pathology reports and physician notes detailing the tumor's location.

• Differentiate from other skin malignancies of the nose, such as squamous cell carcinoma or basal cell carcinoma, which have different code assignments.
• Ensure the pathology report explicitly states "Merkel cell carcinoma" and specifies the nasal site.
• Code additional sites of metastasis separately if documented.