Angiosarcoma of liver

This code identifies a rare and aggressive malignant tumor originating from the endothelial cells lining the blood vessels within the liver. It is a primary hepatic malignancy characterized by rapid growth and a poor prognosis.

Apply this code for documented cases of angiosarcoma specifically affecting the liver. Documentation should clearly state the histological diagnosis of angiosarcoma and specify the liver as the primary site. This code is appropriate when pathology reports confirm the diagnosis.

• Ensure documentation explicitly states "angiosarcoma" and "liver" to avoid confusion with other hepatic malignancies.
• Do not use for metastatic angiosarcoma to the liver; instead, code the primary site and use a secondary malignancy code for the liver.
• Consider sequencing this code as the primary diagnosis when it is the reason for the encounter or admission.