Hepatoblastoma

This code represents hepatoblastoma, a rare malignant liver tumor that primarily affects infants and young children. It originates from immature liver cells and is the most common primary liver cancer in pediatric patients. The tumor can be solitary or multifocal and may be associated with genetic syndromes.

Use this code for confirmed diagnoses of hepatoblastoma based on histopathological examination of biopsy or surgical specimens. It is appropriate for initial diagnosis, treatment planning, and follow-up care for patients with this specific liver malignancy. Documentation should clearly state the diagnosis of hepatoblastoma.

• Ensure documentation specifies "hepatoblastoma" to differentiate from other liver malignancies.
• Consider additional codes for associated genetic syndromes (e.g., Beckwith-Wiedemann syndrome) if present.
• Sequence this code as the primary diagnosis when it is the reason for the encounter.