Atresia and stenosis of large intestine, rectum, and anal canal

This code signifies congenital narrowing or complete absence of a lumen within the large intestine, rectum, or anal canal. These malformations obstruct the normal passage of stool and can lead to significant gastrointestinal distress in newborns.

Apply this code for documented cases of congenital atresia or stenosis affecting any part of the large bowel, rectum, or anus. Documentation should clearly state the specific anatomical site of the obstruction and its congenital nature, often identified shortly after birth due to feeding difficulties, abdominal distension, or failure to pass meconium.

• Differentiate from acquired strictures or obstructions, which are coded differently.
• Ensure documentation specifies the congenital origin; otherwise, consider codes for unspecified intestinal obstruction.
• Review for any associated congenital anomalies that may require additional coding.