Congen absence, atresia and stenosis of rectum w/o fistula

This code signifies a birth defect characterized by the complete absence, abnormal narrowing, or closure of the rectum. This malformation occurs without the presence of an abnormal connection (fistula) between the rectum and another organ or the skin. It represents a severe congenital anomaly affecting the lower gastrointestinal tract.

Use this code for newborns or infants diagnosed with imperforate anus where the rectal pouch ends blindly, or there is a significant stricture, and no associated fistulous tract is identified. Documentation should clearly state the absence of a fistula in addition to the rectal anomaly. This code is appropriate for initial diagnosis and subsequent encounters related to the management of this specific condition.

• Ensure documentation explicitly states "without fistula" to differentiate from codes that include fistulas.
• Consider additional codes for associated congenital anomalies, as these often co-occur.
• Sequence this code as the primary diagnosis when it is the reason for the encounter, especially for surgical correction.