Pemphigoid

This code represents pemphigoid, a group of autoimmune blistering skin diseases characterized by the formation of fluid-filled blisters on the skin and sometimes mucous membranes. These conditions result from an immune response targeting components of the dermal-epidermal junction, leading to separation and blister formation.

Use this code for diagnoses of bullous pemphigoid, cicatricial pemphigoid (mucous membrane pemphigoid), or pemphigoid gestationis. Documentation should clearly state a diagnosis of pemphigoid, often supported by biopsy results showing subepidermal blistering and direct immunofluorescence demonstrating linear deposition of antibodies at the basement membrane zone.

• Differentiate from pemphigus (ICD-9-CM 694.4), which involves intraepidermal blistering.
• Specify the type of pemphigoid if known and documented (e.g., bullous, cicatricial, gestational) for more precise clinical understanding, though this code covers all types.
• Consider additional codes for associated symptoms or complications, such as infections of ruptured blisters.