Other pemphigoid

This code represents various less common forms of pemphigoid, an autoimmune blistering skin disorder, that do not fit into more specific categories like bullous pemphigoid or cicatricial pemphigoid. These conditions are characterized by subepidermal blistering due to autoantibodies targeting components of the dermal-epidermal junction.

Use this code when the physician's documentation specifies a diagnosis of pemphigoid that is not clearly identified as bullous, cicatricial, or another explicitly classified type. This includes conditions such as pemphigoid gestationis, linear IgA bullous dermatosis, or anti-p200 pemphigoid, when a more specific code is unavailable. Documentation should clearly state "other pemphigoid" or a specific variant not otherwise coded.

• Ensure the physician's documentation explicitly rules out bullous pemphigoid (L12.0) or cicatricial pemphigoid (L12.1) before assigning this code.
• Always query the provider for clarification if the type of pemphigoid is ambiguous or if a more specific diagnosis could be obtained.
• Consider additional codes for associated symptoms or complications, such as pruritus (L29.x) or secondary infections (L03.x).