Peripheral autonomic neuropathy in disorders classified elsewhere

This code signifies damage to the peripheral autonomic nervous system that is a manifestation of another underlying disease process. It involves dysfunction of involuntary bodily functions such as heart rate, blood pressure, digestion, and bladder control, occurring secondary to a primary condition.

Apply this code when documentation clearly indicates autonomic neuropathy as a complication or manifestation of a systemic disease, such as diabetes mellitus, amyloidosis, or autoimmune disorders. The medical record must specify that the autonomic neuropathy is peripheral and linked to an "elsewhere classified" condition.

• Always sequence the underlying systemic disease first, as this code is for a manifestation.
• Do not use this code for idiopathic or primary autonomic neuropathies; those have specific codes.
• Ensure the documentation explicitly states "peripheral autonomic neuropathy" and identifies the causative disorder.