Autonomic neuropathy in diseases classified elsewhere

This code signifies damage to the autonomic nervous system that is a manifestation or complication of an underlying disease, but not diabetes. It encompasses conditions where the involuntary bodily functions (e.g., heart rate, digestion, blood pressure) are impaired due to a primary systemic illness.

Apply this code when documentation clearly states "autonomic neuropathy" and specifies an underlying non-diabetic condition, such as amyloidosis, Sjögren's syndrome, or paraneoplastic syndromes. The physician's notes should explicitly link the neuropathy to the primary disease.

• Always sequence the underlying disease code first, as this code is a manifestation code.
• Carefully review documentation to confirm the etiology is not diabetes; if diabetic, use the appropriate E08-E13 code with the .43 subclassification.
• Ensure the provider's documentation clearly establishes the causal link between the underlying disease and the autonomic neuropathy.