Malignant neoplasm of retina

This code signifies a primary cancerous tumor originating in the retina, the light-sensitive tissue at the back of the eye. This condition is a form of intraocular malignancy that can lead to vision loss and, if untreated, can metastasize.

Assign this code for documented cases of primary malignant neoplasm of the retina, such as retinoblastoma in children or less common adult retinal malignancies. Supporting documentation includes pathology reports confirming malignancy and the retinal origin, as well as ophthalmologist notes detailing the diagnosis.

• Differentiate from secondary malignant neoplasms of the retina, which would be coded to a secondary site.
• Ensure documentation specifies the primary nature of the tumor; otherwise, query the provider.
• Consider sequencing rules if the patient has other primary malignancies or complications related to the retinal tumor.