Malignant neoplasm of urachus

This code signifies a primary cancerous tumor originating in the urachus, a remnant of the fetal allantois connecting the bladder to the umbilicus. Urachal carcinoma is a rare but aggressive form of bladder cancer, often presenting with hematuria or abdominal pain.

Apply this code when documentation confirms a malignant neoplasm specifically arising from the urachus, typically identified through biopsy and imaging studies. This diagnosis is often made following cystoscopy and transurethral resection of a bladder mass, with subsequent histopathological confirmation of urachal origin.

• Ensure the pathology report explicitly states the tumor's origin as the urachus, not simply the bladder.
• Distinguish from other bladder malignancies; this code is specific to urachal origin.
• Consider sequencing this code as the primary diagnosis when it is the reason for the encounter.