Congenital complete absence of upper limb, bilateral

This code signifies the complete congenital absence of both upper limbs, meaning the individual was born without either arm. This is a severe birth defect involving the entire upper extremity, from the shoulder to the fingertips, on both sides of the body.

Apply this code when documentation clearly states a bilateral, complete congenital absence of the upper limbs. This diagnosis is typically made at birth or during prenatal imaging. Supporting documentation would include physician notes, imaging reports (e.g., ultrasound), and genetic testing results if performed.

• Ensure documentation specifies "complete" absence and "bilateral" involvement; partial or unilateral absence requires a different code.
• Do not confuse with acquired amputations or other types of limb deficiencies.
• Consider additional codes for any associated congenital anomalies or syndromes.